The disorder

Mechanism & anatomy

Two ways a window can give way — a surge from within or a surge from without. The route predicts the trigger, and the trigger is the clue.

Explosive and implosive routes

Trainee

Goodhill described two routes. The explosive route transmits a CSF pressure surge through the cochlear aqueduct to the perilymph, rupturing the window outward; the implosive route is a middle-ear pressure surge that pushes the window inward.1 Toggle the routes:

CSFcochlear aqueductperilymphround windowmiddle ear (air)
CSF → cochlear aqueduct → inner earA surge in cerebrospinal-fluid pressure (a strain, lift or cough) is transmitted through the cochlear aqueduct to the perilymph, blowing the window membrane OUTWARD into the middle ear.

Where it leaks

The round window is the most frequent site, followed by the oval window (a particular concern after stapes surgery). Microfissures and congenital dehiscences are described too. The anatomy of these windows and the labyrinthine fluids is covered in Anatomy and Physiology. Note the overlap with superior canal dehiscence, which produces pressure/sound sensitivity by a fixed third window rather than a leak.

Why it happens

The commonest clear precipitant is barotrauma (diving, flying); others include head or penetrating trauma, iatrogenic injury after stapes surgery, and congenital malformations such as Mondini dysplasia (which also predisposes to recurrent meningitis). A spontaneous category exists but is the most contested and most likely over-diagnosed.2

Key points

  • Explosive route: a CSF surge via the cochlear aqueduct ruptures the window outward.
  • Implosive route: a middle-ear pressure surge pushes the window inward.
  • The round window is the commonest site; the oval window matters after stapes surgery.
  • Barotrauma, trauma, surgery and congenital malformation are the causes; spontaneous fistula is contested.