The disorder

Clinical features

Four cardinal symptoms, an unmistakable attack, and an audiogram that fluctuates then fixes. Recognising the pattern — and its dangerous late variant — is the heart of the chapter.

The cardinal tetrad

Trainee

Episodic vertigo, fluctuating sensorineural hearing loss, tinnitus and aural fullness — localised to the affected ear — make up the tetrad.1 Not all four need be present at onset; many patients begin with one or two and evolve the full picture.

Episodic vertigo. Spontaneous spinning attacks lasting 20 minutes to 12 hours, with nausea and often vomiting; the patient is usually well between attacks early on.

The arc of an attack

A typical attack runs from a premonitory rise in fullness and tinnitus, through the vertigo crisis, to a long recovery and a quiescent interval. Step through it:

Vertigo crisis · 20 min – 12 h

Sudden severe spinning vertigo with horizontal-torsional nystagmus, nausea and vomiting; the patient is prostrate and cannot function. Lasts 20 minutes to 12 hours — never just seconds, rarely beyond a day.

The fluctuating audiogram

The audiometric signature is a low-frequency sensorineural loss that worsens during attacks and recovers between them, later becoming flat, fixed and severe. Step through the stages, or press Simulate an attack to watch the low frequencies dip and recover:

0204060801002505001k2k4k8kfrequency (Hz)hearing level (dB HL)
Stage 1 · during an attack. 0.5–2 kHz average ≈ 26 dB. Early disease: a low-frequency (rising) loss that worsens during attacks and recovers between them.

The AAO-HNS staging formalises this progression by the four-tone average of the worst audiogram. Cross-reference the live ECochG and VEMP chapters for the electrophysiological correlates.

Variants and Tumarkin drop attacks

Historical variants include cochlear and vestibular Ménière’s (only the auditory or only the vestibular component) and Lermoyez syndrome (hearing improves as vertigo begins).3 The one to know and fear is the Tumarkin otolithic crisis — sudden drop attacks without warning or loss of consciousness, a late-stage feature and a trigger to escalate treatment.

Key points

  • The tetrad: episodic vertigo, fluctuating SNHL, tinnitus and aural fullness in one ear.
  • Attacks last 20 min – 12 h — never seconds, rarely beyond a day.
  • The audiogram shows fluctuating low-frequency SNHL that later fixes and flattens.
  • Tumarkin drop attacks are a dangerous late variant — escalate management.