ECochG Atlas · Compare

Compare diseases

One table, all the disease entities covered in the atlas, set side-by-side on the diagnostic axes that matter for ECochG interpretation: SP/AP behaviour, CM / polarity findings, ABR features, the imaging gold-standard, and the role of ECochG itself. Each disease links back to its full module. See also /cases, /quiz, and /practice.

DiseaseSP/APCM / polarityABRImaging gold-standardRole of ECochG
Ménière's diseaseModule 05Elevated. Ferraro ≥ 0.40, Gibson ≥ 0.30. Misses 30–50% of definite cases.Normal CM, normal polarity behaviour.Normal wave I–V if hearing is preserved; may shrink with severe SNHL.MRI to exclude schwannoma; gadolinium hydrops MRI investigational.Supportive. Adds objective marker of hydrops when clinical picture is consistent.
Superior canal dehiscenceModule 06Elevated. Adams 0.34 cutoff: 92.3% sens, 94% spec. Reversible after plugging.Normal CM. May show enhanced low-frequency response.Normal; SCD does not affect the retrocochlear path.High-resolution temporal-bone CT in the Pöschl plane — gold standard.Adjunct. SP/AP elevation can mimic Ménière's; cVEMP threshold is the functional marker.
Auditory neuropathyModule 07AP absent or severely diminished. SP often preserved → ratio meaningless.CM present and inverts cleanly with polarity reversal (Berlin protocol authenticity).Absent or grossly abnormal despite present CM/OAEs.MRI to exclude cochlear-nerve aplasia/hypoplasia, especially in children.Diagnostic. The polarity-reversal protocol is the definitional test for ANSD.
Sudden SNHLModule 08Variable; no specific signature.Variable; depends on outer-hair-cell status.Threshold elevation tracking the audiogram.MRI within 1–6 months per 2019 AAO-HNSF — excludes schwannoma in 1–7%.Minimal. Not in the modern workup. ABR/MRI carry the diagnostic load.
Perilymph fistulaModule 09May change with intra-test postural manoeuvre (Gibson 1992 protocol).Normal CM/polarity behaviour.Usually normal.CT temporal bone; CTP biochemical assay (where available).Functional test for an active fistula; controversial. Modern alternatives often preferred.
Vestibular schwannomaModule 10Typically normal. A reassuringly normal ECochG never excludes a tumour.Normal CM/polarity.Wave V latency delay, IT5 asymmetry, sometimes wave-V absence — but insensitive.Gadolinium-enhanced MRI — gold standard. No substitute.None as a screening test. AP generator sits peripheral to most schwannomas.
Cochlear synaptopathyModule 11Group-level elevation in the 0.35–0.60 range (Liberman); not an individual diagnostic.Normal CM.Reduced wave-I amplitude at suprathreshold levels — the proposed signature.Not applicable; diagnosis is electrophysiological / behavioural.Research metric. No validated individual clinical use yet.
Intraoperative CIModule 12Not the measure of interest. CM amplitude vs insertion depth is the primary trace.CM recorded via the implant's own electrodes; pattern (stable / drop-recover / progressive drop) is diagnostic.Not used intraoperatively.Postoperative CT for electrode position.Real-time RCT-validated monitoring (Campbell 2022); ≥ 30% drop triggers withdrawal-and-reinsertion.